Changes of a Congenital Nevus of the Vulva after the Beginning of Puberty.

Little is known about the clinical course of genital nevi, particularly congenital ones. We present the case of a girl with a congenital genital nevus that, after the beginning of puberty, doubled its size. The nevus was excised, and histopathology revealed a dysplastic melanocytic nevus with mild and rare severe atypia. Our case illustrates the changes observed in a congenital nevus of the genitalia after puberty, when the genitalia change due to hormonal effects, which occasionally may cause unnecessary anxiety. Moreover, our case underlines the ambiguous histological features of genital nevi in children.