French practical guidelines for the diagnosis and management of idiopathic pulmonary fibrosis - 2021 update. Full-length version.
Обработка статьи · этапы, ошибки и управление
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
Cottin Vincent, Bonniaud Philippe, Cadranel Jacques, Crestani Bruno, Jouneau Stéphane, Marchand-Adam Sylvain, Nunes Hilario, Wémeau-Stervinou Lidwine, Bergot Emmanuel, Blanchard Elodie, Borie Raphaël, Bourdin Arnaud, Chenivesse Cécile, Clément Annick, Gomez Emmanuel, Gondouin Anne, Hirschi Sandrine, Lebargy François, Marquette Charles-Hugo, Montani David, Prévot Grégoire, Quetant Sébastien, Reynaud-Gaubert Martine, Salaun Mathieu, Sanchez Olivier, Trumbic Bruno, Berkani Karim, Brillet Pierre-Yves, Campana Marion, Chalabreysse Lara, Chatté Gérard, Debieuvre Didier, Ferretti Gilbert, Fourrier Jean-Michel, Just Nicolas, Kambouchner Marianne, Legrand Bertrand, Le Guillou Frédéric, Lhuillier Jean-Pierre, Mehdaoui Anas, Naccache Jean-Marc, Paganon Catherine, Rémy-Jardin Martine, Si-Mohamed Salim, Terrioux Philippe, OrphaLung network
Аннотация
METHODS: Practical guidelines were drafted on the initiative of the Coordinating Reference Center for Rare Pulmonary Diseases, led by the French Language Pulmonology Society (SPLF), by a coordinating group, a writing group, and a review group, with the involvement of the entire OrphaLung network, pulmonologists practicing in various settings, radiologists, pathologists, a general practitioner, a health manager, and a patient association. The method followed the "Clinical Practice Guidelines" process of the French National Authority for Health (HAS), including an online vote using a Likert scale.
RESULTS: After a literature review, 54 guidelines were formulated, improved, and then validated by the working groups. These guidelines addressed multiple aspects of the disease: epidemiology, diagnostic procedures, quality criteria and interpretation of chest CT scans, lung biopsy indication and procedures, etiological workup, methods and indications for family screening and genetic testing, assessment of the functional impairment and prognosis, indication and use of antifibrotic agents, lung transplantation, management of symptoms, comorbidities and complications, treatment of chronic respiratory failure, diagnosis and management of acute exacerbations of fibrosis.
CONCLUSION: These evidence-based guidelines are intended to guide the diagnosis and practical management of idiopathic pulmonary fibrosis.