[Chordoma of the ethmoidal sinus. A case report].

Chordomas are dysembryogenic tumors originating from the notochordal process. The case of a 9-month-old male infant with involvement of the ethmoidal sinus and anterior fossa is reported. These tumors are rare in ENT practice and in children arise in the clivus. The diagnosis was made by biopsy, CT and MRI. Surgery is the only effective treatment, with chemotherapy and radiotherapy having little value. The complication and relapse rates are high.