Indian pediatrics · 2014
Severe calcinosis cutis with cutaneous ulceration in juvenile dermatomyositis.
Клинический случайСтатьяНазвание и аннотация: Перевод в очереди
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Meher Bijay Kumar, Mishra Pravakar, Sivaraj Pradeep, Padhan Prasanta
Аннотация
BACKGROUND: Calcinosis cutis is usually seen in long standing and untreated cases of juvenile dermatomyositis.
CASE CHARACTERISTICS: 7-year-old girl with severe calcinosis cutis who developed cutaneous ulceration, rash and myopathy.
OBSERVATION: Myopathic changes in EMG, muscle edema in MRI, elevated muscle enzymes and Jo-1 positive antibodies.
OUTCOME: Treatment with prednisolone and methotrexate resulted in improvement of the lesion.
MESSAGE: Calcinosis cutis may be a presenting feature of juvenile dermatomyositis even in the absence of characteristic findings of rash and weakness.
CASE CHARACTERISTICS: 7-year-old girl with severe calcinosis cutis who developed cutaneous ulceration, rash and myopathy.
OBSERVATION: Myopathic changes in EMG, muscle edema in MRI, elevated muscle enzymes and Jo-1 positive antibodies.
OUTCOME: Treatment with prednisolone and methotrexate resulted in improvement of the lesion.
MESSAGE: Calcinosis cutis may be a presenting feature of juvenile dermatomyositis even in the absence of characteristic findings of rash and weakness.