Ciliary body is not hyperplastic in Weill-Marchesani syndrome.

PURPOSE: To demonstrate the in-vivo morphology of the ciliary body in Weill-Marchesani syndrome which might be of pathophysiological importance for the spherical shape of the crystalline lens.

METHODS

Three juvenile patients with Marchesani syndrome were examined by ultrasound biomicroscopy of the anterior segment.

RESULTS

The in-vivo configuration of the ciliary body in these Weill-Marchesani patients with normal axial length of the eye showed no signs of hyperplasia, and was even relatively small.

CONCLUSION

Spherophakia and hyperplasia of the ciliary body are not necessarily associated with the syndrome, as supposed by Marchesani and other investigators. Instead, spherophakia might be regularly accompanied by a small ciliary body in Weill-Marchesani syndrome.