Congenital Aortic Insufficiency From an Abnormal Left Aortic Cusp Results in Acute Coronary Syndrome.

Acute coronary syndrome (ACS) is a rare presentation in children with isolated congenital aortic insufficiency (AI). We report the case of a six-week-old previously well male who presented with an out-of-hospital cardiac arrest and was diagnosed with severe AI from a left aortic cusp anomaly resulting in ACS. The infant successfully underwent an emergent Ross operation.