[Review of ophthalmologic complications in hereditary bullous epidermolysis. Apropos of 40 cases].

INTRODUCTION

We assessed the frequency of ophthalmologic signs in inherited epidermolysis bullosa and evaluated follow-up.

PATIENTS AND

METHODS

Forty patients were studied retrospectively. Of the 40 patients, 38 had dystrophic and 2 had junctional epidermolysis bullosa. A complete ocular examination was performed in all cases and repeated if necessary (8 times).

RESULTS

Ocular complications were found in 75% of the patients. Corneal anomalies associated or not with refractive anomalies were present. The best corrected visual acuity was less than 3/10 in 20% of the cases. Only 15% had lid modifications.

DISCUSSION: In our series, 75% of the cases had ocular anomalies, similar to other series in the literature. Corneal problems dominated.

CONCLUSION

Ocular lesions in inherited epidermolysis bullosa are often found and require initial ocular examination. Corneal lesions also need to be followed with optical correction to optimize functional prognosis.