[Studies on the function of external respiration in adults and children with anomalous position of the heart chordae].

AIM: To compare respiratory function in adults and children whose heart chordae were in anomalous position (AC) with reference to severity of heart connective tissue dysplasia syndrome.

MATERIALS AND

METHODS

The study included ninety one 6-14-year-olds and 125 adults with AC. The patients were divided into groups by the degree of atrioventricular valvular prolapse (AVVP). External respiration function was examined, and the loop flow-volume was registered by the pulmonological computer system. Inhalation bronchospasmolytic test with berotec was performed.

RESULTS

Tracheobronchial dyskinesia related in degree to AVVP severity was found in 76 and 35% of the adults and children with AC and AVVP, respectively. The berotec test allowed more precise evaluation of tracheobronchial dyskinesia.

CONCLUSION

Functional insufficiency of the connective tissue in patients with cardiac connective tissue dysplasia syndrome progresses with age.