Endodontic management in oculo-facio-cardio-dental syndrome: a case report.

INTRODUCTION

Oculo-facio-cardio-dental (OFCD) syndrome is an X-linked dominant trait. OFCD syndrome is characterized by congenital cataract with secondary glaucoma ocular defects; ventricular and atrial septal defects or mitral valve prolapses; facial traits such as a long narrow face, a high nasal bridge, a bifid nasal tip; and dental anomalies that include radiculomegaly, oligodontia, root dilacerations, malocclusion and delayed eruption. This clinical report describes the endodontic treatment for a 16-year-old girl who suffers from OFCD syndrome.

METHODS

The treatment plan included orthograde re-treatment of #9, #10 with apical plug technique and orthograde retreatment and root canal obturation with modified Thermafil (Dentsply Maillefer, Ballaigues, Switzerland) technique of #21, #22

RESULTS

The modified Thermafil technique makes it possible to reach the working length even in teeth with radiculomegaly.

CONCLUSIONS

Prompt treatment of dental caries make it possible to maintain tooth function and prevent difficult root canal procedures with poor prognoses for success.