Atlanto-axial instability in achondroplastic dwarfs: a report of two cases and literature review.

BACKGROUND

Achondroplasia is the commonest form of human dwarfism. The authors report atlanto-axial instability, in consequence to os odontoideum in this subgroup of patients.

METHODS

Two achondroplastic dwarfs harboring atlanto-axial dislocation are described along with radiological findings.

RESULTS

Both children underwent successful internal rigid immobilization, using sublaminar atlanto-axial wiring.

CONCLUSIONS

Craniovertebral junction instability should be evaluated among these children, whenever foramen magnum insufficiency is being considered.