Brain malformations in linear nevus sebaceous syndrome: an MR study.

A case is presented of a 16-year-old girl who had unilateral linear nevus sebaceous syndrome and ipsilateral brain malformations. These consisted of unilateral megalencephaly, white matter hypoplasia and excessive gray matter, deficient sulcation, and focal areas of pachygyria of the frontal lobe best seen on magnetic resonance imaging.