Results of total correction in complete atrioventricular septal defects with congenital or surgically induced right ventricular outflow tract obstruction.

The outcome of total repair in 29 children who had complete atrioventricular septal defect (AVSD) and congenital or surgically induced right ventricular outflow tract obstruction (RVOTO) is reviewed. All 11 patients with congenital RVOTO had normal pulmonary artery (PA) pressure before the complete repair. Of the 18 children who had undergone PA banding, seven had PA pressure above 30 mm Hg (mean, 53.5). Two had elevated pulmonary vascular resistance (greater than 3 units). Early mortality was 18.2% for the patients with congenital RVOTO and 44.4% for those who had undergone PA banding (p not significant). After a mean follow-up of 5 years, the results are good in the survivors of both groups. Analysis of multiple-risk factors indicate that, for the total group of patients, death was significantly more common in children less than 5 years of age (p less than 0.01) or less than 15 kg (p less than 0.02) than in older or larger patients.