Segmental hypoplasia of the kidney in children.

Of 36 cases of segmental hypoplasia of the kidney in children and adolescents anatomic lesions are described and a detailed definition of the abnormality is given. The disease occurs predominantly in girls and show no familial tendency. Segmental hypoplasia may be separated into four groups: (1) unilateral, (2) bilateral and asymmetrical, (3) bilateral and symmetrical, and (4) unusual presentation such as latent disease or association with other anomalies. The importance of differentiating these four groups is indicated not only with respect to the clinical course and prognosis but also with regard to treatment.