Internal medicine (Tokyo, Japan) · 2013
Pulmonary hypertension and refractory heart failure in a patient with Crow-Fukase (POEMS) syndrome.
Клинический случайСтатьяНазвание и аннотация: Перевод в очереди
Обработка статьи · этапы, ошибки и управление
Загрузка состояния…
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
Yokokawa Tetsuro, Nakazato Kazuhiko, Kanno Yuki, Mizukami Hiroyuki, Kobayashi Atsushi, Yoshihisa Akiomi, Takahashi Hiroshi, Shichishima-Nakamura Akiko, Ohkawara Hiroshi, Noji Hideyoshi, Suzuki Hitoshi, Saitoh Shu-ichi, Ogawa Kazuei, Hisa Shinichi, Takeishi Yasuchika
Аннотация
We experienced the case of a 67-year-old man with refractory heart failure. He presented with dyspnea and progressive pitting edema of the lower limbs. Diuretics were insufficient to improve his symptoms. Cardiac catheterization demonstrated pulmonary hypertension. Additional examinations confirmed polyneuropathy, organomegaly, endocrinopathy and monoclonal gammopathy. The plasma vascular endothelial growth factor (VEGF) level was 1,340 pg/mL. The patient was diagnosed with Crow-Fukase (POEMS) syndrome. Echocardiography detected left ventricular hypertrophy and diastolic dysfunction. Polysomnography demonstrated severe sleep-disordered breathing. We herein describe a case of pulmonary hypertension with Crow-Fukase syndrome accompanied by left ventricular diastolic dysfunction and sleep-disordered breathing.
Предметные рубрики MeSH
AgedDexamethasoneDiureticsDrug ResistanceEdemaFurosemideHeart FailureHumansHypertension, PulmonaryHypertrophy, Left VentricularMaleMelphalanPOEMS SyndromePolysomnographyPrednisolonePulmonary Wedge PressureSleep Apnea SyndromesThalidomideUltrasonographyVascular Endothelial Growth Factor AVentricular Dysfunction, Left