[Surgical results of Fontan procedure in hypoplastic left heart syndrome].

BACKGROUND

We reviewed the preoperative hemodynamic factors, surgical results and intermediate outcome of Fontan procedure in hypoplastic left heart syndrome (HLHS).

METHOD: From 1990 to 2006, 34 patients with HLHS completed Fontan procedure in our hospital. We compared preoperative hemodynamic factors, surgical results and postoperative course between HLHS group and functional single right ventricle (SRV) group who had undergone Fontan procedure. In addition, influence of the initial palliation [Norwood procedure with modified Blalock-Taussig (BT) shunt, Norwood procedure with right ventricle (RV)-pulmonary artery (PA) conduit and bilateral PA banding] to surgical results and postoperative course was investigated.

RESULTS

The PA index was smaller in HLHS group than SRV group but there was no difference in surgical results and intermediate outcome between the 2 groups. Although age at Fontan was older in Norwood with BT shunt, preoperative hemodynamic factors, surgical results and intermediate outcome were similar between the 3 groups.

CONCLUSION

Although the PA index in HLHS group was small, the surgical results of Fontan procedure in HLHS group were comparable with those in SRV group. The surgical result of Fontan procedure was satisfactory irrespective of the initial palliative procedure.