[Malformation syndrome with constriction rings, pseudoligaments, acral defects and syndactylism: diagnosis and treatment (author's transl)].

Congenital constricting bands of the extremities, pseudo-ligaments, distal defects of fingers and syndacatyly are all characteristic marks of this syndrome. At least two of the features must be present to make the diagnosis. The authors' results are reported and experience in paediatric hand surgery is essential. This should be performed as early as possible. Operative techniques are described.