Posterior fossa epidermoid in a member of a kindred with von Hippel-Lindau disease.

The authors describe the case of a middle-aged member of a kindred with von Hippel-Lindau disease in whom a posterior fossa epidermoid developed. The epidermoid was initially thought to be a hemangioblastoma, a tumor to which those who have von Hippel-Lindau disease are predisposed. Radiologic investigations, especially magnetic resonance imaging, were useful in demonstrating the extra-axial nature of the tumor and also in characterizing it as an epidermoid.