Heart (British Cardiac Society) · 2016
A 12-year-old boy with chest pain and dyspnoea.
Клинический случайСтатьяНазвание и аннотация: Перевод в очереди
Обработка статьи · этапы, ошибки и управление
Загрузка состояния…
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
Latorre Navarro Libertad, García-Guereta Silva Luis, Ruíz Bravo-Burguillos Elena
Аннотация
CLINICAL INTRODUCTION: A previously healthy 12-year-old boy presented with chest pain and dyspnoea. ECG (figure 1), echocardiogram (figure 2) and myocardial MRI (figure 3) were performed.Electromyography revealed mild proximal weakness. Blood tests showed creatine kinase 997 UI/L, aspartate transaminase 398 UI/L, alanine transaminase 293 UI/L and lactate deshidrogenase 1730 UI/L. Ophthalmology test showed diffuse loss of pigment in the retinal pigment epithelium. Myocardial biopsy was performed (figure 4). A cardiomyopathy was suspected. LAMP2 gene was sequenced, and a stop mutation was identified.
QUESTION: What is the most likely diagnosis suggested based on the patient's tests and history? Danon's disease.Fabry's disease.Hypertrophic cardiomyopathy.Noonan's syndrome.Pompe's disease.
QUESTION: What is the most likely diagnosis suggested based on the patient's tests and history? Danon's disease.Fabry's disease.Hypertrophic cardiomyopathy.Noonan's syndrome.Pompe's disease.
Предметные рубрики MeSH
Angina PectorisBiopsyChildDNA Mutational AnalysisDyspneaEchocardiographyElectrocardiographyGlycogen Storage Disease Type IIbHumansHypertrophy, Left VentricularLysosomal-Associated Membrane Protein 2Magnetic Resonance ImagingMaleMutationStroke VolumeVentricular Dysfunction, LeftVentricular Function, LeftVentricular Remodeling