[Translation and validation of the Egen Klassifikation scale for the Spanish population: functional assessment for non-ambulatory individuals with Duchenne's muscular dystrophy and spinal muscular atrophy].

INTRODUCTION

The Egen Klassifikation (EK) scale is a questionnaire that assesses the functional capacity of people with Duchenne muscular dystrophy and spinal muscular atrophy who can't walk and use a wheelchair.

AIM: To translate and validate the scale for the Spanish population as a tool for measuring functional capacity in these patients.

PATIENTS AND

METHODS

We performed first a translation-back translation of EK in the Spanish population and subsequently practiced reliability study of Spanish translated version of the scale. It held three measurements in 30 patients aged 4 to 67 years. Two of these measurements were performed by the same observer, and the third by a second observer to assess intra- and inter-observer agreement.

RESULTS

The values refer to the total score of the scale items, EK sum, and reflect a reliability index of 0.995. They also show a higher reliability to 0.86 in each of the items in both intra- and inter-observations observer.

CONCLUSIONS

The Spanish version of the EK is a valid and reliable instrument for the Spanish population as a tool for measuring functional capacity in patients with Duchenne muscular dystrophy and spinal muscular atrophy are not ambulatory and use a wheelchair.