[Scrotum-perineal granular cell tumor in pediatric age: A case report.].

OBJECTIVE

Report a case of a scrotum-perinea lGranular Cell Tumor (GCT) in pediatric age.

METHODS

To report a case.

RESULTS

A 12 years old men with a multiple GCT history, located in both extremities, abdomen and scrotum perineal region. Surgical excision of all lesions and a genetic studyare performed to rule out Noonan syndrome.

CONCLUSION

GCT or Abrikossoff tumor is a tumor witha very low incidence, especially in pediatric age. The most frequent form of presentation a solitary nodule and the most common behavior is in the form of a benign tumor. Immunohistochemistryis crucial for its diagnosis, the main characteristicis positivity for the S100 protein. Although scrotal location is very rare, it must be considered in the differential diagnosis of scrotal mass. Surgical excision is the treatment of choice.