Dysplasia Epiphysealis Hemimelica Treated with Osteochondral Allograft: A Case Report.

BACKGROUND

Dysplasia epiphysealis hemimelica (DEH), or Trevor's disease, is a developmental disorder of the pediatric skeleton characterized by asymmetric osteochondral overgrowth.

METHODS

We present the case of a five year old boy with a two year history of right knee pain and evidence of DEH on imaging who underwent initial arthroscopic resection of his lesion with subsequent recurrence. The patient then underwent osteochondral allograft revision surgery and was asymptomatic at two year follow-up with a congruent joint surface.

RESULTS

To our knowledge, this is the first reported case of a DEH lesion treated with osteochondral allograft and also the youngest reported case of osteochondral allograft placement in the literature.

CONCLUSIONS

Osteochondral allograft may be a viable option in DEH and other deformities of the pediatric knee.

LEVEL OF EVIDENCE: Level V.