Improving oral health-related quality of life for a child with Hunter's syndrome: A case report and review of literature.

INTRODUCTION

Hunter's syndrome (HS) is a severe metabolic disorder with heterogeneous multisystemic manifestations including orodental features. The heterogeneity of manifestations of HS, complicate the provision of proper dental care.

CASE REPORT: A 12 years old male was diagnosed with HS and referred for a comprehensive oral rehabilitation after he failed to receive proper dental care. He was complaining of fractured infected central incisors due to trauma, multiple caries, and poor oral hygiene. Despite his negative behaviour and poor dental history, dental treatment was provided under local anesthesia, using basic behaviour guidance techniques. The treatment outcomes had a positive impact on his behavior toward dental treatment and his oral health. During the first year follow up, there was a significant improve in his oral health-related quality of life assessed by Early Childhood Oral Health Impact Scale (ECOHIS) questionnaire.

CONCLUSION

This report highlighted the importance of proper referral and treatment of the necessary dental needs for patients with HS. Pediatric dentists need to work together with pediatricians to promote oral health, and formulate educational programs to eliminate barriers to necessary dental care suitable for each patient's need.