Hemophilia and von Willebrand Disease: A Review of Emergency Department Management.

BACKGROUND

Hemophilia and von Willebrand disease (VWD) are the most common congenital coagulation factor deficiencies. Patients with these disorders who experience bleeding complications are often initially managed in the emergency department (ED).

OBJECTIVE OF THE REVIEW: This review will focus on the emergency department management of patients with these disorders and provide an update on current treatment options.

DISCUSSION: The mainstay of management is initial stabilization, control of bleeding when possible, and administration of specific factors. Early coordination of care with hematology is critical.

CONCLUSIONS

Emergency medicine providers must have an understanding of the pathophysiology, clinical presentation, and management strategies in order to optimally care for these complex patients.