World neurosurgery · 2019
Case of Hemorrhagic Moyamoya Disease Associated with Von Willebrand Disease.
Клинический случайСтатьяНазвание и аннотация: Перевод пока не подготовлен
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Suzuki Yume, Shiba Masato, Wada Hideo, Yasuda Ryuta, Toma Naoki, Suzuki Hidenori
Аннотация
BACKGROUND: Association of moyamoya disease (MMD) with von Willebrand disease (vWD) is extremely rare.
CASE DESCRIPTION: We first report a 27-year-old female case of MMD concurrent with vWD type 1, which presented as hemorrhagic stroke. The patient underwent a revascularization surgery with perioperative replacement therapy of von Willebrand factor and coagulation factor VIII. No hemorrhagic complications occurred.
CONCLUSIONS: The patient overcame postoperative transient neurological events and fully recovered. We discuss appropriate perioperative supplementation of coagulation factors for a revascularization surgery for MMD with vWD.
CASE DESCRIPTION: We first report a 27-year-old female case of MMD concurrent with vWD type 1, which presented as hemorrhagic stroke. The patient underwent a revascularization surgery with perioperative replacement therapy of von Willebrand factor and coagulation factor VIII. No hemorrhagic complications occurred.
CONCLUSIONS: The patient overcame postoperative transient neurological events and fully recovered. We discuss appropriate perioperative supplementation of coagulation factors for a revascularization surgery for MMD with vWD.