[The Vogt-Koyanagi-Harada syndrome in 11-year-old girl].

PURPOSE: The Vogt-Koyanagi-Harada syndrome is an idiopathic, multisystem disorder which typically affects pigmented individuals between 20-50 years old. The typical symptoms include granulomatous panuveitis with characteristic extraocular dermato-neurological manifestations. The case of VKH syndrome affecting Polish girl is very rare.

CASE REPORT: A 11-year-old girl had an important decrease of visual acuity in both eyes (RE 0.1 and LE 0.2), with the presence of bullous serous retinal detachment in both eyes. Besides, in right eye some keratic precipitates were noted. The routine laboratory evaluation failed to provide a diagnosis. The patient was treated with an intravenous bolus of corticosteroid therapy and then, high dose of oral prednisone.

RESULTS

After administered therapy the visual acuity improved rapidly in both eyes (RE 1.0 and LR 0.9), and the exudative retinal detachment resolved. After 5 months, the patient's examination showed a sunset glow fundus with several whitish rounded lesions in peripheral fundus, which is typical for the VKH syndrome.

CONCLUSIONS

The VKH syndrome rarely affects young children, so the diagnosis may be difficult in the absence of the typical extraocular manifestations. In such atypical cases the diagnosis is based on the clinical evolution of the disease.