Anesthetic implications for patients with Segawa syndrome.

STUDY

OBJECTIVE

To characterize the perioperative course of patients with Segawa syndrome undergoing anesthetic management.

DESIGN

Retrospective observational case study.

SETTING

Large tertiary medical center.

PATIENTS: Patients with Segawa syndrome who underwent procedures requiring anesthetic management at our institution from January 1, 2004, through July 31, 2015.

MEASUREMENTS: The health records of patients with Segawa syndrome.

MAIN

RESULTS

Twelve patients with Segawa syndrome underwent 25 procedures requiring anesthetic management, including 20 operations with general anesthesia. Succinylcholine was administered in 6 cases and nondepolarizing neuromuscular blockers in 5 cases, all without adverse effects. Perioperative complications were unrelated to anesthetic management or underlying neurologic condition. In 16 operations, the patients were receiving levodopa therapy at the time of the procedure.

CONCLUSIONS

In this cohort, patients with Segawa syndrome tolerated the anesthetic management, including neuromuscular blocker administration. Although these patients are frequently receiving levodopa therapy, no associated complications were noted.