[Retroperitoneal fibrosis in children].

The authors describe retroperitoneal fibrosis (RPF) in general and the case of a six-year-old child who suffered from RPF. Due to the atypical course of the disease the diagnosis was very difficult not only due to the clinical course but also because of the histological examination. The atypical course was manifested by affection of the lungs, liver, pancreas and porta hepatis. The urinary system was also affected by the fibrotic disease. The authors reached the conclusion that in an atypical course of the disease only repeated biopsy is decisive for establishment of the diagnosis.