Revue neurologique · 2008
[Polyradiculopathy revealing an enteropathy associated T-cell lymphoma in a patient with celiac disease].
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Jousserand G, Poujois A, Antoine J-C, Camdessanché J-P
Аннотация
INTRODUCTION: Celiac disease (CD) may be complicated by an enteropathy associated T-cell lymphoma (EATL), but lymphomatous dissemination outside the gastrointestinal tract is uncommon especially to the peripheral nervous sytem.
OBSERVATION: We report a 54-year-old CD patient with EATL revealed by subacute polyradiculopathy.
DISCUSSION: Peripheral neuropathies associated with CD are generally not polyradiculopathies, but sensorimotor neuropathies. Peripheral neurological complications of non-Hodgkin lymphoma are more frequent with B-lymphoma and a neurological presentation of EATL is very rare.
CONCLUSION: This case illustrates the usefulness of searching for EATL in CD patients with polyradiculopathy.
OBSERVATION: We report a 54-year-old CD patient with EATL revealed by subacute polyradiculopathy.
DISCUSSION: Peripheral neuropathies associated with CD are generally not polyradiculopathies, but sensorimotor neuropathies. Peripheral neurological complications of non-Hodgkin lymphoma are more frequent with B-lymphoma and a neurological presentation of EATL is very rare.
CONCLUSION: This case illustrates the usefulness of searching for EATL in CD patients with polyradiculopathy.