Acta oto-laryngologica · 2026
Hearing rehabilitation in patients with Treacher Collins syndrome.
СтатьяОбзорНазвание и аннотация: Перевод в очереди
Обработка статьи · этапы, ошибки и управление
Загрузка состояния…
Ошибки и ограничения
История · было → стало
Состояние обновляется каждые 5 секунд, пока блок открыт. Процент показывается только там, где известен объём работы. Пауза останавливает продолжение этапа; текущий запрос к источнику может завершиться.
Guo Qianhui, Zhu Jikai, Wang Danni, Zhao Shouqin
Аннотация
BACKGROUND: Patients with Treacher Collins syndrome primarily have bilateral conductive hearing loss, accompanied by severe craniofacial anomalies. The selection of appropriate management is essential.
OBJECTIVES: To explore the suitable hearing reconstruction methods in patients with Treacher Collins syndrome (TCS).
MATERIAL AND METHODS: A retrospective study was conducted on 14 TCS patients by collecting the medical history, audiological, and imaging results. The sound field and speech recognition ability from 7 follow-up patients with and without the bone conduction hearing aid (BCHA) were measured.
RESULTS: The HRCT anatomical variations showed facial nerve displacement (92.31%), high jugular bulb (61.54%), Low-lying middle cranial fossa (53.85%), anteriorly located sigmoid sinus (11.54%), vestibular window abnormalities(76.92%), and stenosis with cholesteatoma(30.77%). The unilateral BCHA implantation markedly improved the average sound field threshold from 62.00 ± 4.00 dB HL to 35.71 ± 4.99 dB HL with significant gains in SRT and SRS. However, hearing improvement was limited in stenosis patients with cholesteatoma after canalplasty and tympanoplasty. Postoperative complications included one case of canal restenosis and two cases of implant failure.
CONCLUSIONS AND SIGNIFICANCE: The BCHA can provide sufficient hearing gain and represent the preferred hearing intervention in TCS patients.
OBJECTIVES: To explore the suitable hearing reconstruction methods in patients with Treacher Collins syndrome (TCS).
MATERIAL AND METHODS: A retrospective study was conducted on 14 TCS patients by collecting the medical history, audiological, and imaging results. The sound field and speech recognition ability from 7 follow-up patients with and without the bone conduction hearing aid (BCHA) were measured.
RESULTS: The HRCT anatomical variations showed facial nerve displacement (92.31%), high jugular bulb (61.54%), Low-lying middle cranial fossa (53.85%), anteriorly located sigmoid sinus (11.54%), vestibular window abnormalities(76.92%), and stenosis with cholesteatoma(30.77%). The unilateral BCHA implantation markedly improved the average sound field threshold from 62.00 ± 4.00 dB HL to 35.71 ± 4.99 dB HL with significant gains in SRT and SRS. However, hearing improvement was limited in stenosis patients with cholesteatoma after canalplasty and tympanoplasty. Postoperative complications included one case of canal restenosis and two cases of implant failure.
CONCLUSIONS AND SIGNIFICANCE: The BCHA can provide sufficient hearing gain and represent the preferred hearing intervention in TCS patients.