Histology of alveolar bone and primary tooth roots in a case of cleidocranial dysplasia.

Cleidocranial dysplasia is commonly reported as an autosomal dominant inherited condition with defective formation of clavicles, malformation of the craniofacial bones, very slow exfoliation of the primary teeth and failure of the eruption of the permanent dentition. Lack of clinical resorption of the roots of the deciduous teeth and/or surrounding bone, lead to eruption failure of permanent teeth. Histopathological study (light and scanning electron microscopy), in a case of cleidocranial dysplasia, gives prominence to the hypothesis of abnormal remodelling of bone and cementum.