Management of myoepithelioma of the vulva--case report and review of the literature.

Myoepithelioma of the vulva is a rare condition, with only three cases having been reported so far. As a consequence it is quite difficult to decide on the appropriate management due to the paucity of data. We present our case together with a review of all relevant literature in order to collect and summarise the experience accrued so far, and draw conclusions regarding the management of these myoepitheliomas when they appear on the vulva. It seems that vulval myoepitheliomas can be of low- or high-grade malignancy and that the grade, which determines the prognosis, should be the main factor to consider when planning the management. We also conclude that the clinical behaviour of these tumours of the vulva most probably follow the course of the myoepitheliomas that affect the soft tissues in general.