[Mondini's deafness].

Mondini's deafness was the congenital malformation of inner ear. We studied 199 ears of 106 cases. Most of them were found deaf when they were babies. High resolution computed tomography of temperal bone was described: cochlea malformation 4 ears; malformation of cochlea, vestibule and semicircular canal 90 ears; vestibular of semicircular malformation without cochlea malformation 105 ears, this type was called the vestibule malformation or untypically Mondini's. Of all the 199 ears there were 81 ears with enlargement of the vestibule aqueducts. The pathogeny, clinical manifestation and treatment were discussed.