[Osteogenesis imperfecta. The effect of intramedullary nails in long tubular bones].

INTRODUCTION

The aim of the study was to describe the clinical, radiological, and functional results of intramedullary nailing of deformities in the lower extremities of children with osteogenesis imperfecta after the use of multiple osteotomies and non-telescoping rods (rush pins).

MATERIAL AND

METHODS

Eight children with osteogenesis imperfecta, who consecutively underwent surgery during 1991-1994, were entered in the study.

RESULTS

Sixteen operations were performed on eight children: 12 on the femur and four on the tibia. Like others, we found a high complication rate, 50%. Radiological correction of angular deformities was good. The functional outcome was satisfactory and the patients were satisfied.

CONCLUSION

Correction and stabilisation of deformities in the lower extremities in children with osteogenesis imperfecta with the use of non-telescoping rods is an acceptable method of decreasing fractures and allowing most formerly non-ambulatory children to walk. Furthermore, the cosmetics were improved.